Dari millist sebelah, semoga bermanfaat. Fera <[EMAIL PROTECTED]> wrote:Saya juga baru tau ada sindrom ini, jadi ini hanya info buat semuanya.
dari medicastore.com : NAMA Sindroma Kawasaki DEFINISI Sindroma Kawasaki (Sindroma Kelenjar Getah Bening Mukokutaneus, Poliarteritis Infantil) adalah suatu penyakit non-spesifik, tanpa agen infeksius tertentu, yang menyerang selaput lendir, kelenjar getah bening, lapisan pembuluh darah dan jantung. PENYEBAB Penyebabnya tidak diketahui.Sindroma Kawasaki pertama kali ditemukan di Jepang pada akhir tahun 1960. Penyakit ini menyerang anak berumur 2 bulan sampai 5 tahun dan 2 kali lebih sering ditemukan pada anak laki-laki. GEJALA Gejalanya berupa: - Demam yang turun-naik, tetapi biasanya diatas 39° Celsius, sifatnya menetap (lebih dari 5 hari) dan tidak memberikan respon terhadap asetaminofen maupun ibuprofen dalam dosis normal - Rewel, tampak mengantuk - Kadang timbul nyeri kram perut - Ruam kulit di batang tubuh dan di sekeliling daerah yang tertutup popok - Ruam pada selaput lendir (misalnya lapisan mulut dan vagina) - Tenggorokan tampak merah - Bibir merah, kering dan pecah-pecah - Lidah tampak merah (strawberry-red tongue) - Kedua mata menjadi merah, tanpa disertai keluarnya kotoran - Telapak tangan dan telapak kaki tampak merah, tangan dan kaki membengkak - Kulit pada jari tangan dan jari kaki mengelupas (pada hari ke 10-20) - Pembengkakan kelenjar getah bening leher - Nyeri persendian (atralgia) dan pembengkakan, seringkali simetris (pada sisi tubuh kiri dan kanan). KOMPLIKASI Sekitar 5-20% penderita mengalami komplikasi jantung, yang biasanya timbul pada minggu ke 2-4: · Peradangan arteri koroner (arteri yang membawa darah ke jantung) · Aneurisma (pelebaran bagian dari arteri koroner) · Perikarditis (peradangan kantung jantung) · Miokarditis akut (peradangan otot jantung) · Gagal jantung · Kematian otot jantung (infark miokardium). Komplikasi lainnya: · Ruam yang tidak biasa uveitis anterior) · Nyeri atau peradangan sendi (terutama sendi-sendi yang kecil) · Peradangan non-infeksius pada selaput otak (meningitis aseptik) · Peradangan kandung empedu · Diare. DIAGNOSA Diagnosis ditegakkan jika terjadi demam selama lebih dari 5 hari dan ditemukan 4 dari 5 gambaran berikut: - Ruam kulit - Alat gerak (lengan dan tungkai ) merah dan membengkak - Mata merah - Perubahan pada bibir dan mulut - Pembengkakan kelenjar getah bening. Pemeriksaan yang biasa dilakukan: · EKG dan ekokardiografi, bisa menunjukkan tanda-tanda dari miokarditis, perikarditis, artritis, meningitis aseptik atau vaskulitis koroner · Hitung darah lengkap (menunjukkan peningkatan jumlah sel darah putih dan anemia (berkurangnya jumlah sel darah merah); pemeriksaan darah berikutnya menunjukkan peningkatan jumlah trombosit · Rontgen dada · Analisa air kemih (bisa menunjukkan adanya nanah atau protein dalam air kemih). PENGOBATAN Pengobatan dini secara berarti dapat mengurangi resiko terjadinya kerusakan pada arteri koroner dan mempercepat pemulihan demam, ruam dan rasa tidak nyaman. Selama 1-4 hari diberikan immunoglobulin dosis tinggi melalui infus dan aspirin dosis tinggi melalui mulut. Setelah demam turun, biasanya aspirin dalam dosis yang lebih rendah diberikan selama beberapa bulan untuk mengurangi resiko kerusakan arteri koroner dan pembentukan bekuan darah. Dilakukan beberapa kali pemeriksaan EKG untuk mendeteksi adanya komplikasi jantung. Aneurisma yang besar diobati dengan aspirin dan obat anti pembekuan (misalnya warfarin). Aneurisma yang kecil cukup diatasi dengan aspirin. Jika anak menderita influenza atau cacar air, untuk mengurangi resiko terjadinya sindroma Reye, sebaiknya untuk sementara waktu diberikan dipiridamol, bukan aspirin. PROGNOSIS Jika tidak terjadi komplikasi jantung, biasanya akan terjadi pemulihan sempurna. Sekitar 1-2% penderita meninggal, biasanya akibat komplikasi jantung; 50% diantaranya meninggal pada bulan pertama, 75% meninggal pada bulan kedua, 95% meninggal pada bulan keenam. Tetapi kematian bisa terjadi 10 tahun kemudian dan kadang secara tiba-tiba. Aneurisma yang kecil cenderung menghilang dalam waktu 1 tahun, tetapi arteri koroner tetap lemah sehingga beberapa tahun kemudian timbul kelainan jantung. ----------------------------------------------------------------------- -----Original Message----- From: Patricia Soetjipto [mailto:[EMAIL PROTECTED] Sent: Wednesday, September 29, 2004 3:11 PM Kawazaki pertama kali ditemukan tahun 1967. Ini saya postkan artikelnya dari www.americanheart.org: Kawasaki Disease What is Kawasaki disease? Kawasaki (KAH'wah-SAH'ke) disease is a children's illness. It's also known as Kawasaki syndrome or mucocutaneous (mu"ko-ku-TA'ne-us) lymph node syndrome. It and acute rheumatic (roo-MAT'ik) fever are the two leading causes of acquired heart disease in children in the United States. Who gets Kawasaki disease? About 80 percent of the people with Kawasaki disease are under age five. Children over age eight are rarely affected. The disease occurs more often among boys (63 percent) and among those of Asian ancestry. But it can occur in every racial and ethnic group. Up to 2,500 cases of Kawasaki disease are being diagnosed annually in the United States. Less than 1 percent of those who get it die. What happens to those with Kawasaki disease? The symptoms of Kawasaki disease include... fever, rash swollen hands and feet irritation and redness of the whites of the eyes swollen lymph glands in the neck irritation and inflammation of the mouth, lips and throat Doctors don't know what causes Kawasaki disease, but it doesn't seem to be hereditary or contagious. Scientists who've studied it think the evidence strongly suggests it's caused by an infectious agent such as a virus. It's very rare for more than one child in a family to develop Kawasaki disease. Less than 2 percent of children have another attack of Kawasaki disease. In as many as 20 percent of the children with Kawasaki disease, the heart is affected. The coronary arteries or the heart muscle itself can be damaged. How does Kawasaki disease affect the heart? The coronary arteries are most often affected. Part of a coronary wall can be weakened and balloon (bulge out) in an aneurysm. A blood clot can form in this weakened area and block the artery, sometimes leading to a heart attack. The aneurysm can also burst, but this rarely happens. Other changes include inflammation of the heart muscle (myocarditis) or the sac surrounding the heart (pericarditis). Arrhythmias (abnormal heart rhythms) or abnormal functioning of some heart valves also can occur. Usually all the heart problems go away in five or six weeks, and there's no lasting damage. Sometimes coronary artery damage persists, however. An arrhythmia or damaged heart muscle can be detected using an electrocardiogram (EKG). An echocardiogram (or "echo") is used to look for possible damage to the heart or coronary arteries. How is Kawasaki disease treated? Even though the cause of Kawasaki disease is unknown, certain medicines are known to help. Aspirin is often used to reduce fever, rash, joint inflammation and pain, and to help prevent blood clots from forming. Another medicine, intravenous gamma globulin, can decrease the risk of developing coronary artery abnormalities when given early in the illness. TIME Vision : To be a well respected Indonesian company that delivers the widest range of leading international brands of timepieces, lifestyle products and services. TIME Mission : We offer excellent products and services to satisfy our customers and partners, while enhancing our employees' well being as well as contributing to society. Disclaimer. This e-mail is confidential and legally privileged. If you are not the intended recipient, please advise the sender and delete this e-mail. 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